Diagnosis classification
TheInternational Classification of Diseases for Oncology (ICD-O ) is a domain-specific extension of theInternational Statistical Classification of Diseases and Related Health Problems fortumor diseases. This classification is widely used bycancer registries .
It is currently in its third revision (ICD-O-3). ICD-10 includes a list of morphology codes. They stem from ICD-O second edition (ICD-O-2) that was valid at the time of publication.
The classification has two axes: topography and morphology.
Themorphology axis addresses the microscopic structure (histology ) of the tumor.
This axis has particular importance because theSystematized Nomenclature of Medicine ("SNOMED") has adopted the ICD-O classification of morphology. SNOMED has been changing continuously, and several different versions of SNOMED are in use. Accordingly, mapping of ICD-O codes to SNOMED requires careful assessment of whether entities are indeed true matches.
Thetopography axis addresses the tumor's site in the body. It is standardized with the C section ofICD-10 .
There were no changes in the topography axis between ICD-O-2 and ICD-O-3.
SeeList of ICD-10 codes#(C00–C97) Malignant Neoplasms for examples.
International Classification of Diseases for Oncology, Third Edition (ICD-O-3)[ edit ] 5th Digit Behaviour Code for Neoplasms [ edit ] /0 Benign/1 Uncertain whether benign or malignant/2 Carcinoma in situ /3 Malignant, primary site/6 Malignant ,metastatic siteMalignant, secondary site /9 Malignant, uncertain whether primary or metastatic site Morphology Codes (ICD-O-3)[ edit ] Source:[ 1]
M8000/0 Neoplasm ,benign
M8000/1 Neoplasm , uncertain whetherbenign ormalignant
Neoplasm , NOSTumor, NOS Unclassified tumor, uncertain whether benign or malignant Unclassified tumor, borderline malignancy M8000/3 Neoplasm ,malignant
Tumor, malignant, NOS Malignancy Cancer Unclassified tumor, malignant Blastoma , NOSM8000/6 Neoplasm ,metastatic
Neoplasm, metastatic Tumor, metastatic Tumor, secondary Tumor embolus M8000/9 Neoplasm ,malignant , uncertain whether primary ormetastatic
Unclassified tumor, malignant, uncertain whether primary or metastatic M8001/0 Tumor cells ,benign
M8001/1 Tumor cells , uncertain whetherbenign ormalignant
M8001/3 Tumor cells ,malignant
M8002/3 Malignant tumor ,small cell type
M8003/3 Malignant tumor ,giant cell type
M8004/3 Malignant tumor ,spindle cell type
Malignant tumor, fusiform cell type M8005/0 Clear cell tumor ,NOS
M8005/3 Malignant tumor ,clear cell type
M8010/0 Epithelial tumor ,benign M8010/2 Carcinoma in situ, NOSM8010/3 Carcinoma , NOSEpithelial tumor, malignant M8010/6 Carcinoma, metastatic, NOSM8010/9 Carcinomatosis M8011/0 Epithelioma , benignM8011/3 Epithelioma, malignantM8012/3 Large cell carcinoma, NOSM8013/3 Large cell neuroendocrine carcinoma M8014/3 Large cell carcinoma withrhabdoid phenotype M8015/3 Glassy cell carcinoma M8020/3 Carcinoma, undifferentiated, NOSM8021/3 Carcinoma, anaplastic, NOSM8022/3 Pleomorphic carcinoma M8030/3 Giant cell andspindle cell carcinoma M8031/3 Giant cell carcinoma M8032/3 Spindle cell carcinoma, NOSM8033/3 Pseudosarcomatous carcinoma M8034/3 Polygonal cell carcinoma M8035/3 Carcinoma withosteoclast -like giant cellsM8040/0 Tumorlet , benignM8040/1 Tumorlet, NOSM8041/3 Small cell carcinoma , NOSM8042/3 Oat cell carcinoma (C34._)M8043/3 Small cell carcinoma,fusiform cell M8044/3 Small cell carcinoma, intermediate cellM8045/3 Combined small cell carcinomaM8046/3 Non-small cell carcinoma (C34._) 805–808 Squamous Cell Neoplasms[ edit ] M8050/0 Papilloma, NOS(except papilloma of bladder M8120/1) M8050/2 Papillary carcinoma in situM8050/3 Papillary carcinoma, NOSM8051/0 Verrucous papillomaM8051/3 Verrucous carcinoma, NOSCondylomatous carcinoma Verrucous squamous cell carcinoma Verrucous epidermoid carcinoma Warty carcinoma M8052/0 Squamous cell papilloma, NOSSquamous papilloma Keratotic papilloma M8052/2 Papillary squamous cell carcinoma, non-invasivePapillary squamous cell carcinoma in situ M8052/3 Papillary squamous cell carcinomaPapillary epidermoid carcinoma M8053/0 Squamous cell papilloma, invertedM8060/0 Squamous papillomatosisM8070/2 Squamous cell carcinoma in situ, NOSEpidermoid carcinoma in situ, NOS Intraepidermal carcinoma, NOS Intraepithelial squamous cell carcinoma M8070/3 Squamous cell carcinoma, NOSEpidermoid carcinoma, NOS Squamous carcinoma Squamous cell epithelioma M8070/6 Squamous cell carcinoma, metastatic, NOSM8071/3 Squamous cell carcinoma, keratinizing, NOSSquamous cell carcinoma, large cell, keratinizing Epidermoid carcinoma, keratinizing M8072/3 Squamous cell carcinoma, large cell, nonkeratinizing, NOSSquamous cell carcinoma, non keratinizing, NOS Epidermoid carcinoma, large cell, nonkeratinizing M8073/3 Squamous cell carcinoma, small cell, nonkeratinizingEpidermoid carcinoma, small cell, nonkeratinizing M8074/3 Squamous cell carcinoma, spindle cellEpidermoid carcinoma, spindle cell Squamous cell carcinoma, sarcomatoid M8075/3 Squamous cell carcinoma, adenoidSquamous cell carcinoma, pseudoglandular Squamous cell carcinoma, acantholytic M8076/2 Squamous cell carcinoma in situ with questionable stromal invasionEpidermoid carcinoma in situ with questionable stromal invasion M8076/3 Squamous cell carcinoma, microinvasiveM8077/2 Squamous intraepithelial neoplasia, grade IIICervical intraepithelial neoplasia, grade III (C53._)CIN III, NOS (C53._) CIN III with severe dysplasia (C53._) Vaginal intraepithelial neoplasia, grade III (C52._) Vulvar intraepithelial neoplasia, grade III (C51._) Anal intraepithelial neoplasia, grade III (C21.1) M8078/3 Squamous cell carcinoma with horn formationM8080/2 Queyrat erythroplasia (C60._)M8081/2 Bowen disease (C44._)Intraepidermal squamous cell carcinoma, Bowen type (C44._) M8082/3 Lymphoepithelial carcinomaLymphoepithelioma Lymphoepithelioma-like carcinoma Schmincke tumor (C11._) M8083/3 Basaloid squamous cell carcinomaM8084/3 Squamous cell carcinoma, clear cell typeM8090/1 Basal cell tumor (C44._)(M8090/3 )Basal cell carcinoma , NOS (C44._)Basal cell epithelioma Rodent ulcer Pigmented basal cell carcinoma M8091/3 Multifocal superficial basal cell carcinoma (C44._)Multicentric basal cell carcinoma M8092/3 Infriltrating basal cell carcinoma, NOS (C44._)Infiltrating basal cell carcinoma, non-sclerosing Infiltrating basal cell carcinoma, sclerosing Basal cell carcinoma, morphoeic Basal cell carcinoma, desmoplastic type M8093/3 Basal cell carcinoma, fibroepithelial (C44._)Fibroepithelioma of Pinkus type Fibroepithelial basal cell carcinoma, Pinkus type Pinkus tumor Fibroepithelioma, NOS M8094/3 Basosquamous carcinoma (C44._)Mixed basal-squamous cell carcinoma M8095/3 Metatypical carcinomaM8096/0 Intraepidermal epithelioma of Jadassohn (C44._)M8097/3 Basal cell carcinoma, nodular (C44._)Basal cell carcinoma, micronodular M8098/3 Adenoid basal carcinoma (C53._)M8100/0 Trichoepithelioma (C44._)Brooke tumor Epithelioma adenoides cysticum M8101/0 Trichofolliculoma (C44._)M8102/0 Trichilemmoma (C44._)M8102/3 Trichilemmocarcinoma (C44._)M8103/0 Pilar tumor (C44._)Proliferating trichilemmal cyst Proliferating trichilemmal tumor M8110/0 Pilomatrixoma, NOS (C44._)Calcifying epithelioma of Malherbe Pilomatricoma, NOS M8110/3 Pilomatrix carcinoma (C44._)Pilomatrixoma, malignant Pilomatricoma, malignant Matrical carcinoma M8120/0 Transitional cell papilloma, benignM8120/1 Urothelial papilloma, NOSPapilloma of bladder (C67._) Transitional cell papilloma, NOS M8120/2 Transitional cell carcinoma in situUrothelial carcinoma in situ M8120/3 Transitional cell carcinoma, NOSUrothelial carcinoma, NOS Transitional carcinoma M8121/0 Schneiderian papilloma, NOS (C30.0, C31._)Sinonasal papilloma, NOS Sinonasal papilloma, exophytic Sinonasal papilloma, fungiform Transitional cell papilloma, inverted, benign Transitional papilloma, inverted, benign M8121/1 Transitional cell papilloma, inverted, NOSTransitional papilloma, inverted, NOS Schneiderian papilloma, inverted Columnar cell papilloma Cylindrical cell papilloma Oncocytic Schneiderian papilloma M8121/3 Schneiderian carcinoma (C30.0, C31._)Cylindrical cell carcinoma M8122/3 Transitional cell carcinoma, spindle cellTransitional cell carcinoma, sarcomatoid M8123/3 Basaloid carcinomaM8124/3 Cloacogenic carcinoma (C21.2)M8130/1 Papillary transitional cell neoplasm of low malignant potential (C67._)Papillary urothelial neoplasm of low malignant potential M8130/2 Papillary transitional cell carcinoma, non-invasive (C67._)Papillary urothelial carcinoma, non-invasive M8130/3 Papillary transitional cell carcinoma (C67._)Papillary urothelial carcinoma M8131/3 Transitional cell carcinoma, micropapillary ( C67._)(M8140/0 )Adenoma , NOS M8140/1 Atypical adenomaBronchial adenoma, NOS (C34._) M8140/2 Adenocarcinoma in situ, NOS(M8140/3 )Adenocarcinoma , NOS M8140/6 Adenocarcinoma, metastatic, NOSM8141/3 Scirrhous adenocarcinomaScirrhous carcinoma Carcinoma with productive fibrosis (M8142/3 )Linitis plastica (C16._) M8143/3 Superficial spreading adenocarcinomaM8144/3 Adenocarcinoma, intestinal type (C16._)Carcinoma, intestinal type M8145/3 Carcinoma, diffuse type (C16._)Adenocarcinoma, diffuse type M8146/0 Monomorphic adenomaM8147/0 Basal cell adenomaM8147/3 Basal cell adenocarcinomaM8148/2 Glandular intraepithelial neoplasia, grade IIIProstatic intraepithelial neoplasia, grade III (C61.9) M8149/0 Canalicular adenomaM8150/0 Islet cell adenoma (C25._)Islet cell tumor, benign Nesidioblastoma Islet cell adenomatosis M8150/1 Islet cell tumor, NOS (C25._)M8150/3 Islet cell carcinoma (C25._)Islet cell adenocarcinoma (M8151/0 )Insulinoma , NOS (C25._) M8151/3 Insulinoma, malignant (C25._)Beta cell tumor, malignant (M8152/0 )Glucagonoma , NOS (C25._) M8152/3 Glucagonoma, malignant (C25._)Alpha cell tumor, malignant (M8153/1 )Gastrinoma , NOSG cell tumor, NOS Gastrin cell tumor M8153/3 Gastinoma, malignantG cell tumor, malignant Gastrin cell tumor, malignant M8154/3 Mixed islet cell and exocrine adenocarcinoma (C25._)Mixed acinar-endocrine carcinoma Mixed ductal-endocrine carcinoma M8155/1 Vipoma, NOS(M8155/3 )Vipoma , malignant M8156/1 Somatostatinoma, NOSSomatostatin cell tumor, NOS M8156/3 Somatostatinoma, malignantsomatostatin cell tumor, malignant M8157/1 Enteroglucagonoma, NOSM8157/3 Enteroglucagonoma, malignantM8160/0 Bile duct adenoma (C22.1, C24.0)(M8160/3 )Cholangiocarcinoma (C22.1, C24.0)Bile duct carcinoma Bile duct adenocarcinoma M8161/0 (C22.1, C24.0)M8161/3 Bile duct cystadenocarcinoma (C22.1, C24.0)M8162/3 Klatskin tumor (C22.1, C24.0)M8170/0 Liver cell adenoma (C22.0)(M8170/3 )Hepatocellular carcinoma , NOS (C22.0)Liver cell carcinoma Hepatocarcinoma Hepatoma, malignant Hepatoma, NOS M8171/3 Hepatocellular carcinoma, fibrolamellar (C22.0)M8172/3 Hepatocellular carcinoma, scirrhous (C22.0)Sclerosing hepatic carcinoma M8173/3 Hepatocellular carcinoma, spindle cell variant (C22.0)Hepatocellular carcinoma, sarcomatoid M8174/3 Hepatocellular carcinoma, clear cell type (C22.0)M8175/3 Hepatocellular carcinoma, pleomorphic typeM8180/3 Combined hepatocellular carcinoma and cholangiocarcinoma (C22.0)Mixed hepatocellular and bilde duct carcinoma Hepatocholangiocarcinoma M8190/0 Trabecular adenomaM8190/3 Trabecular adenocarcinomaM8191/0 Embryonal adenomaM8200/0 Eccrine dermal cylindroma (C44._)Turban tumor Cylindroma of skin (M8200/3 )Adenoid cystic carcinoma Adenocystic carcinoma Cylindroma, NOS(except cylindroma of skin M8200/0) Adenocarcinoma, cylindroid Bronchial adenoma, cylindroid (C34._) M8201/2 Cribiform carcinoma in situ (C50._)Ductal carcinoma in situ, cribiform type M8201/3 Cribiform carcinoma, NOSDuctal carcinoma, cribiform type M8202/0 Microcystic adenoma (C25._)M8204/0 Lactating adenomaM8210/0 Adenomatous polyp, NOSM8210/2 Adenocarcinoma in situ in adenomatous polypAdenocarcinoma in situ in tubular adenoma Carcinoma in situ in adenomatous polyp Adenocarcinoma in situ in polypoid adenoma Adenocarcinoma in situ in a polyp, NOS Carcinoma in situ in a polyp, NOS M8210/3 Adenocarcinoma in adenomatous polypAdenocarcinoma in tubular adenoma Carcinoma in adenomatous polyp Adenocarcinoma in polypoid adenoma Adenocarcinoma in a polyp, NOS Carcinoma in a polyp, NOS M8211/0 Tubular adenoma, NOSM8211/3 Tubular adenocarcinomaM8212/0 Flat adenomaM8213/0 Serrated adenoma (C18._)Mixed adenomatous and hyperplastic polyp M8214/3 Parietal cell carcinoma (C16._)Parietal cell adenocarcinoma M8215/3 Adenocarcinoma of anal glands (C21.1)Adenocarcinoma of anal ducts M8220/0 Adenomatous polyposis coli (C18._)Familial polyposis coli Adenomatosis, NOS M8220/3 Adenocarcinoma in adenomatous polyposisM8221/0 Multiple adenomatous polypsM8221/3 Adenocarcinoma in multiple adenomatous polypsM8230/2 Ductal carcinoma in situ, solid type (C50._)Intraductal carcinoma, solid type M8230/3 Solid carcinoma, NOSSolid carcinoma with mucin formation Solid adenocarcinoma with mucin formation M8231/3 Carcinoma simplex(M8240/1 ) Carcinoid tumor of uncertain malignant potentialCarcinoid tumor, NOS, ofappendix (C18.1)Carcinoid, NOS, of appendix Carcinoid tumor, argentaffin, NOS Argentaffinoma, NOS M8240/3 Carcinoid tumor, NOS(except of appendix M8240/1) Carcinoid, NOS(except of appendix) Typical carcinoid Bronchial adenoma, carcinoid M8241/3 Enterochromaffin cell carcinoidCarcinoid tumor, argentaffin, malignant Argentaffinoma, malignant EC cell carcinoid Serotonin producing carcinoid M8242/1 Enterochromaffin-like cell carcinoid, NOSM8242/3 Enterochromaffin-like cell tumor, malignantECL cell carcinoid, malignant M8243/3 Goblet cell carcinoidMucocarcinoid tumor Mucinous carcinoid M8244/3 Composite carcinoidCombined carcinoid and adenocarcinoma Mixed carcinoid-adenocarcinoma M8245/1 Tubular carcinoidM8245/3 Adenocarcinoid tumorM8246/3 Neuroendocrine carcinoma, NOSM8247/3 Merkel cell carcinoma (C44._)Merkel cell tumor Primary cutaneous neuroendocrine carcinoma M8248/1 ApudomaM8249/3 Atypical carcinoid tumorM8250/1 Pulmonary adenomatosis (C34._)M8250/3 Bronchiolo-alveolar adenocarcinoma, NOS (C34._)Bronchiolo-alveolar carcinoma, NOS Bronchiolar adenocarcinoma Bronchiolar carcinoma Alveolar cell carcinoma M8251/0 Alveolar adenoma (C34._)M8251/3 Alveolar adenocarcinoma (C34._)M8252/3 Bronchiolo-alveolar carcinoma, non-mucinous (C34._)Bronchiolo-alveolar carcinoma, Club cell Bronchiolo-alveolar carcinoma, type II pneumocyte M8253/3 Bronchiolo-alveolar carcinoma, mucinous (C32._)Bronchiolo-alveolar carcinoma, goblet cell type M8254/3 Bronchiolo-alveolar carcinoma, mixed mucinous and non-mucinous (C34._)Bronchiolo-alveolar carcinoma, Club cell and goblet cell type Bronchiolo-alveolar carcinoma, type II pneumocyte and goblet cell type Bronchiolo-alveolar carcinoma, indeterminate type M8255/3 Adenocarcinoma combined with mixed subtypesAdenomcarcinoma combined with other types of carcinoma M8260/0 Papillary adenoma, NOSM8260/3 Papillary adenocarcinoma, NOSPapillary carcinoma of thyroid (C73.9) Papillary renal cell carcinoma (C64.9) M8261/0 Villous adenoma, NOSM8261/2 Adenocarcinoma in situ in villous adenomaM8261/3 Adenocarcinoma in villous adenomaM8262/3 Villous adenocarcinomaM8263/0 Tubulovillous adenoma, NOSvilloglandular adenoma Papillotubular adenoma M8263/2 Adenocarcinoma in situ in tubulovillous adenomaM8263/3 Adenocarcinoma in tubulovillous adenomaPapillotubular adenocarcinoma Tubulopapillary adenocarcinoma M8264/0 Papillomatosis, glandularBiliary papillomatosis (C22.1, C24.0) M8270/0 Chromophobe adenoma (C75.1)M8270/3 Chromophobe carcinoma (C75.1)Chromophobe adenocarcinoma (M8271/0 )Prolactinoma (C75.1) M8272/0 Pituitary adenoma, NOS (C75.1)M8272/3 Pituitary carcinoma, NOS (C75.1)M8280/0 Acidophil adenoma (C75.1)M8280/3 Acidophil carcinoma (C75.1)Acidophil adenocarcinoma Eosinophil carcinoma Eosinophil adenocarcinoma M8281/0 Mixed acidophil-basophil adenoma (C75.1)(M8290/0 ) Oxyphilic adenoma M8290/3 Oxyphilic adenocarcinomaOncocytic carcinoma Oncocytic adenocarcinoma Hurthlecell carcinoma (C73.9) Hurthle cell adenocarcinoma Follicular carcinoma, oxyphilic cell (C73.9) M8300/0 Basophil adenoma (C75.1)M8300/3 Basophil carcinoma (C75.1)Basophil adenocarcinoma Mucoid cell adenocarcinoma M8310/0 Clear cell adenomaM8310/3 Clear cell adenocarcinoma, NOSClear cell carcinoma Clear cell adenocarcinoma, mesonephroid M8311/1 Hypernephroid tumor(M8312/3 )Renal cell carcinoma , NOS (C64.9) M8313/0 Clear cell adenofibroma (C56.9)clear cell cystadenofibroma M8313/1 Clear cell adenofibroma of borderline malignancyClear cell cystadenofibroma of borderline malignancy M8313/3 Clear cell adenocarcinofibroma (C56.9)Clear cell cystadenocarcinofibroma M8314/3 Lipid-rich carcinoma (C50._)M8315/3 Glycogen-rich carcinomaM8316/3 Cyst-associated renal cell carcinoma (C64.9)M8317/3 Renal cell carcinoma, chromophobe type (C64.9)Chromophobe cell renal carcinoma M8318/3 Renal cell carcinoma, sarcomatoid (C64.9)Renal cell carcinoma, spindle cell M8319/3 collecting duct carcinoma (C64.9)Bellini duct carcinoma Renal carcinoma, collecting duct type M8320/3 Granular cell carcinomaGranular cell adenocarcinoma M8321/0 Chief cell adenoma (C75.0)M8322/0 Water-clear cell adenoma (C75.0)M8322/3 Water-clear cell adenocarcinoma (C75.0)Water-celar cell carcinoma M8323/0 Mixed cell adenomaM8323/3 Mixed cell adenocarcinomaM8324/0 LipoadenomaM8325/0 Metanephric adenoma (C64.9)M8330/0 Follicular adenoma (C73.9)M8330/1 Atypical follicular adenoma (C73.9)M8330/3 Follicular adenocarcinoma, NOS (C73.9)Follicular carcinoma, NOS M8331/3 Follicular adenocarcinoma, well differentiated (C73.9)Follicular carcinoma, well differentiated M8332/3 Follicular adenocarcinoma, trabecular (C73.9)Follicular carcinoma, trabecular Follicular adenocarcinoma, moderately differentiated FOlloicular carcinoma, moderately differentiated M8333/0 Microfollicular adenoma, NOS (C73.9)M8333/3 Fetal adenocarcinomaM8334/0 Macrofollicular adenoma (C73.9)M8335/3 Follicular carcinoma, minimally invasive (C73.9)Follicular carcinoma, encapsulated M8336/0 Hyalinizing trabecular adenoma (C73.9)(M8337/3)Insular carcinoma (C73.9) M8340/3 Papillary carcinoma, follicular variant (C73.9)Papillary adenocarcinoma, follicular variant Papillary and follicular adenocarcinoma Papillary and follicular carcinoma M8341/3 Papillary microcarcinoma (C73.9)M8342/3 Papillary carcinoma, oxyphilic cell (C73.9)M8343/3 Papillary carcinoma, encapsulated (C73.9)M8344/3 Papillary carcinoma, columnar cell (C73.9)Papillary carcinoma, tall cell M8345/3 Medullary carcinoma with amyloid stroma (C73.9)Parafollicular cell carcinoma C cell carcinoma M8346/3 Mixed medullary-follicular carcinoma (C73.9)M8347/3 Mixed medullary-papillary carcinoma (C73.9)M8350/3 Nonencapsulated sclerosing carcinoma (C73.9)Nonencapsulated sclerosing adenocarcinoma Nonencapsulated sclerosing tumor Papillary carcinoma, diffuse sclerosing M8360/1 Multiple endocrine adenomasM8361/0 Juxtaglomerular tumor (C64.9)M8370/0 Adrenal cortical adenoma, NOS (C74.0)Adrenal cortical tumor, benign Adrenal cortical tumor, NOS M8370/3 Adrenal cortical carcinoma (C74.0)Adrenal cortical adenocarcinoma Adrenal cortical tumor, malignant M8371/0 Adrenal cortical adenoma, compact cell (C74.0)M8372/0 Adrenal cortical adenoma, pigmented (C74.0)Black adenoma Pigmented adenoma M8373/0 Adrenal cortical adenoma, clear cell (C74.0)M8374/0 Adrenal cortical adenoma, glomerulosa cell (C74.0)M8375/0 Adrenal cortical adenoma, mixed cell (C74.0)(M8380/0 )Endometrioid adenoma , NOSEndometrioid cystadenoma, NOS M8380/1 Endometrioid adenoma, borderline malignancyEndometrioid cystadenoma, borderline malignancy Endometrioid tumor of low malignant potential Atypical proliferative endometrioid tumor M8380/3 Endometrioid adenocarcinoma, NOSEndometrioid carcinoma, NOS Endometrioid cystadenocarcinoma M8381/0 Endometrioid adenofibroma, NOSEndometrioid cystadenofibroma, NOS M8381/1 Endometrioid adenofibroma, borderline malignancyEndometrioid cystadenofibroma, borderline malignancy M8381/3 Endometriod adenofibroma, malignantEndometrioid cystadenofibroma, malignant M8382/3 Endometrioid adenocarcinoma, secretory variantM8383/3 Endometrioid adenocarcinoma, ciliated cell variantM8384/3 Adenocarcinoma, endocervical typeM8390/0 Skin appendage adenoma (C44._)
Skin appendage tumor, benign Adnexal tumor, benign M8390/3 Skin appendage carcinoma (C44._)
M8391/0 Follicular fibroma (C44._)
Trichodiscoma Fibrofolliculoma Perifollicular fibroma M8392/0 Syringofibroadenoma (C44._)
M8400/0 Sweat gland adenoma (C44._)
Sweat gland tumor, benign Hidradenoma, NOS Syringadenoma, NOS M8400/1 Sweat gland tumor, NOS (C44._)
M8400/3 Sweat gland adenocarcinoma (C44._)
Sweat gland carcinoma Sweat gland tumor, malignant M8401/0 Apocrine adenoma
M8401/3 Apocrine adenocarcinoma
M8402/0 Nodular hidradenoma (C44._)
Eccrine acrospiroma Clear cell hidradenoma M8402/3 Nodular hidradenoma, malignant (C44._)
M8403/0 Eccrine spiradenoma (C44._)
M8403/3 Malignant eccrine spiradenoma (C44._)M8404/0 Hidrocystoma (C44._)
M8405/0 Papillary hidradenoma
M8406/0 Papillary syringadenoma (C44._)
Papillary syringocystadenoma Syringocystadenoma papilliferum M8407/0 Syringoma, NOS (C44._)
M8407/3 Sclerosing sweat duct carcinoma (C44._)
Syringomatous carcinoma Microcystic adnexal carcinoma M8408/0 Eccrine papillary adenoma (C44._)
M8408/1 Aggressive digital papillary adenoma (C44._)
M8408/3 Eccrine papillary adenocarcinoma (C44._)
Digital papillary adenocarcinoma M8409/0 Eccrine poroma (C44._)
M8410/0 Sebaceous adenoma (C44._)
M8410/3 Sebaceous adenocarcinoma (C44._)
M8413/3 Eccrine adenocarcinoma (C44._)
M8420/0 Ceruminous adenoma (C44.2)
M8420/3 Ceruminous adenocarcinioma (C44.2)
M8430/1 Mucoepidermoid tumor
M8430/3 Mucoepidermoid carcinoma
M8440/0 Cystadenoma , NOS
M8440/3 Cystadenocarcinoma, NOS
M8441/0 Serous cystadenoma, NOS
Serous cystoma Serous microcystic adenoma M8441/3 Serous cystadenocarcinoma, NOS (C56.9)
Serous adenocarcinoma, NOS Serous carcinoma, NOS M8442/1 Serous cystadenoma, borderline malignancy (C56.9)
Serous tumor, NOS, of low malignant potential Atypical proliferating serous tumor M8443/0 Clear cell cystadenoma (C56.9)
M8444/1 Clear cell cystic tumor of borderline malignancy (C56.9)
Atypical proliferating clear cell tumor M8450/0 Papillary cystadenoma, NOS (C56.9)
M8450/3 Papillary cystadenocarcinoma, NOS (C56.9)
Papillocystic adenocarcinoma M8451/1 Papillary cystadenoma, borderline malignancy (C56.9)
M8452/1 Solid pseudo papillary tumor (C25._)
Papillary cystic tumor Solid and papillary epithelial neoplasm Solid and cystic tumor M8452/3 Solid pseudopapillary carcinoma (C25._)
M8453/0 Intraductal papillary-mucinous adenoma (C25._)
M8453/1 Intraductal papillary-mucinous tumor with moderate dysplasia (C25._)
M8453/2 Intraductal papillary-mucinous carcinoma, non-invasive (C25._)
M8453/3 Intraductal papillary-mucinous carcinoma invasive (C25._)
M8454/0 Cystic tumor of atrio-ventricular node (C38.0)
M8460/0 Papillary serous cystadenoma, NOS (C56.9)
M8460/3 Papillary serous cystadenocarcinoma (C56.9)
Papillary serous adenocarcinoma Micropapillary serous carcinoma M8461/0 Serous surface papilloma (C56.9)
M8461/3 Serous surface papillary carcinoma (C56.9)
Primary serous papillary carcinoma of peritoneum (C48.1) M8462/1 Serous papillary cystic tumor of borderline malignancy (C56.9)
Papillary serous cystadenoma, borderline malignancy Papillary serous tumor of low malignant potential Atypical proliferative papillary serous tumor M8463/1 Serous surface papillary tumor of borderline malignancy (C56.9)
M8470/0 Mucinous cystadenoma, NOS (C56.9)
Mucinous cystoma Pseudomucinous cystadenoma, NOS M8470/1 Mucinous cystic tumor with moderate dysplasia (C25._)
M8470/2 Mucinous cystadenocarcinoma, non-invasive (C25._)
M8470/3 Mucinous cystadenocarcinoma/ NOS (C56.9)
Pseudomucinous adenocarcinoma Pseudomucinous cystadenocarcinoma, NOS M8471/0 Papillary mucinous cystadenoma, NOS (C56.9)
Papillary pseudomucinous cystadenoma, NOS M8471/3 papillary mucinous cystadenocarcinoma (C56.9)
Papillary pseudomucinous cystadenocarcinoma M8472/1 Mucinous cystic tumor of borderline malignancy (C56.9)
Mucinous cystadenoma, borderline malignancy Pseudomucinous cystadenoma, borderline malignancy Mucinous tumor, NOS, of low malignant potential Atypical proliferative mucinous tumor M8473/1 Papillary mucinous cystadenoma, borderline malignancy (C56.9)
Papillary pseudomucinous cystadenoma borderline malignancy Papillary mucinous tumor of low malignant potential M8480/0 Mucinous adenoma
M8480/3 Mucinous adenocarcinoma
Mucinous carcinoma Colloid adenocarcinoma Colloid carcinoma Gelatinous adenocarcinoma Gelatinous carcinoma Mucoid adenocarcinoma Mucoid carcinoma Mucous adenocarcinoma Mucous carcinoma Pseudomyxoma peritonei with unknown primary site (C80.9) M8480/6 Pseudomyxoma peritonei
M8481/3 Mucin-producing adenocarcinoma
Mucin-producing carcinoma Mucin-secreting adenocarcinoma Mucin-secreting carcinoma M8482/3 Mucinous adenocarcinoma, endocervical type
M8490/3 Signet ring cell carcinoma
Signet ring cell adenocarcinoma M8490/6 Metastatic signet ring cell carcinoma
M8500/2 Intraductal carcinoma, noninfiltrating, NOS
Intraductal adenocarcinoma, noninfiltrating, NOS Intraductal carcinoma, NOS Ductal carcinoma in situ, NOS (C50._) DCIS, NOS Ductal intraepithelial neoplasia 3 DIN 3 M8500/3 Infiltrating duct carcinoma, NOS (C50._)
Infiltrating duct adenocarcinoma Duct adenocarcinoma, NOS Duct carcinoma, NOS Duct cell carcinoma Ductal carcinoma, NOS M8501/2 Comedocarcinoma, noninfiltrating (C50._)
Ductal carcinoma in situ, comedo type DCIS, comedo type M8501/3 Comedocarcinoma, NOS (C50._)
M8502/3 Secretory carcinoma of breast (C50._)
Juvenile carcinoma of breast M8503/0 Intraductal papilloma
Duct adenoma, NOS Ductal papilloma M8503/2 Noninfiltrating intraductal papillary adenocarcinoma (C50._)
Noninfiltrating intraductal papillary carcinoma Intraductal papillary adenocarcinoma, NOS Intraductal papillary carcinoma, NOS Ductal carcinoma in situ, papillary DCIS, papillary M8503/3 Intraductal papillary adenocarcinoma with invasion (C50._)
Infiltrating papillary adenocarcinoma Infiltrating and papillary adenocarcinoma M8504/0 Intracystic papillary adenoma
M8504/2 Noninfiltrating intracystic carcinoma
M8504/3 Intracystic carcinoma, NOS
Intracystic papillary adenocarcinoma M8505/0 Intraductal papillomatosis, NOS
Diffuse intraductal papillomatosis M8506/0 Adenoma of nipple (C50._)
Subareolar duct papillomatosis M8507/2 Intraductal micropapillary carcinoma (C50._)
Ductal carcinoma in situ, micropapillary Intraductal carcinoma, clinging M8508/3 Cystic hypersecretory carcinoma (C50._)
M8510/3 Medullary carcinoma, NOS
M8512/3 Medullary carcinoma with lymphoid stroma
M8513/3 Atypical medullary carcinoma (C50._)
M8514/3 Duct carcinoma, desmoplastic type
M8520/2 Lobular carcinoma in situ, NOS (C50._)
Lobular carcinoma, noninfiltrating LCIS, NOS M8520/3 Lobular carcinoma, NOS (C50._)
Lobular adenocarcinoma Infiltrating lobular carcinoma, NOS M8521/3 Infiltrating ductular carcinoma (C50._)
M8522/2 Intraductal carcinoma and lobular carcinoma in situ (C50._)
M8522/3 Infiltrating duct and lobular carcinoma (C50._)
Lobular and ductal carcinoma Infiltrating duct and lobular carcinoma in situ Intraductal and lobular carcinoma Infiltrating lobular carcinoma and ductal carcinoma in situ M8523/3 Infiltrating duct mixed with other types of carcinoma (C50._)
Infiltrating duct and cribiform carcinoma Infiltrating duct and mucinous carcinoma Infiltrating duct and tubular carcinoma Infiltrating duct and colloid carcinoma M8524/3 Infiltrating lobular mixed with other types of carcinoma (C50._)
M8525/3 Polymorphous low grade adenocarcinoma
Terminal duct adenocarcinoma M8530/3 Inflammatory carcinoma (C50._)
Inflammatory adenocarcinoma M8540/3 Paget disease, mammary (C50._)
M8541/3 Paget disease and infiltrating duct carcinoma of breast (C50._)
M8542/3 Paget disease, extramammary(except Paget disease of bone)
M8543/3 Paget disease and intraductal carcinoma of breast (C50._)
M8550/0 Acinar cell adenoma
Acinar adenoma Acinic cell adenoma M8550/1 Acinar cell tumor
M8550/3 Acinar cell carcinoma
Acinic cell adenocarcinoma Acinar adenocarcinoma Acinar carcinoma M8551/3 Acinar cell cystadenocarcinoma
M8560/0 Mixed squamous cell and glandular papilloma
M8560/3 Adenosquamous carcinoma
Mixed adenocarcinoma and squamous cell carcinoma Mixed adenocarcinoma and epidermoid carcinoma M8561/0 Adenolymphoma (C07._, C08._)
M8562/3 Epithelial-myoepithelial carcinoma
M8570/3 Adenocarcinoma with squamous metaplasia
M8571/3 Adenocarcinoma with cartilaginous and osseous metaplasia
Adenocarcinoma with cartilaginous metaplasia Adenocarcinoma with osseous metaplasia M8572/3 Adenocarcinoma with spindle cell metaplasia
M8573/3 Adenocarcinoma with apocrine metaplasia
Carcinoma with apocrine metaplasia M8574/3 Adenocarcinoma with neuroendocrine differentiation
Carcinoma with neuroendocrine differentiation M8575/3 Metaplastic carcinoma, NOS
M8576/3 Hepatoid adenocarcinoma
858 Thymic Epithelial Neoplasms [ edit ] M8580/0 Thymoma , benign (C37.9)M8580/1 Thymoma, NOS (C37.9)M8580/3 Thymoma, malignant, NOS (C37.9)M8581/1 Thymoma, type A, NOS (C37.9)Thymoma, spindle cell, NOS Thymoma, medullary, NOS M8581/3 Thymoma, type A, malignant (C37.9)
Thymoma, spindle cell, malignant Thymoma, medullary, malignant M8582/1 Thymoma, type AB, NOS (C37.9)
M8582/3 thymoma, type AB, malignant (C37.9)
Thymoma, mixed type, malignant M8583/1 Thymoma, type B1, NOS (C37.9)
Thymoma, lymphocyte-rich, NOS Thymoma, lymphocytic, NOS Thymoma, predominantly cortical, NOS Thymoma, organoid, NOS M8583/3 Thymoma, type B1, malignant (C37.9)
Thymoma, lymphocyte-rich, malignant Thymoma, lymphocytic, malignant Thymoma, predominantly cortical, malignant Thymoma, organoid, malignant M8584/1 Thymoma, type B2, NOS (C37.9)
M8584/3 Thymoma, type B2, malignant (C37.9)
Thymoma, cortical, malignant M8585/1 Thymoma, type B3, NOS (C37.9)
Thymoma, epithelial, NOS Thymoma, atypical, NOS M8585/3 Thymoma, type B3, malignant (C37.9)
Thymoma, epithelial, malignant Thymoma, atypical, malignant Well differentiated thymic carcinoma M8586/3 Thymic carcinoma, NOS (C37.9)
M8587/0 Ectopic hamartomatous thymoma
M8588/3 Spindle epithelial tumor with thymus-like element
Spindle epithelial tumor with thymus-like differentiation SETTLE M8589/3 Carcinoma showing thymus-like element
Carcinoma showing thymus-like differentiation CASTLE M8590/1 Sex cord-stromal tumor , NOS
Sex cord/gonadal stromal tumor, NOS Testicular/ovarian stromal tumor M8591/1 Sex cord-gonadal stromal tumor, incompletely differentiated
M8592/1 Sex cord-gonadal stromal tumor, mixed forms
M8593/1 Stromal tumor with minor sex cord elements
M8600/0 Thecoma , NOS
M8600/3 Thecoma, malignant
M8601/0 Thecoma, luteinized
M8602/0 Sclerosing stromal tumor
M8610/0 Luteoma, NOS
M8620/1 Granulosa cell tumor , NOS
M8620/3 Granulosa cell tumor, malignant
Granulosa cell carcinoma Granulosa cell tumor, sarcomatoid M8621/1 Granulosa cell-theca cell tumor
Theca cell-granulosa cell tumor M8622/1 Granulosa cell tumor, juvenile
M8623/1 Sex cord tumor with annular tubules
M8630/1 Androblastoma/Arrhenoblastoma, benign
M8630/1 Androblastoma/Arrhenoblastoma , NOS
M8630/3 Androblastoma/Arrhenoblastoma , malignant
M8631/0 Sertoli-Leydig cell tumor , well differentiated
M8631/1 Sertoli-Leydig cell tumor of intermediate differentiation
M8631/3 Sertoli-Leydig cell tumor , poorly differentiated
M8632/1 Gynandroblastoma
M8633/1 Sertoli-Leydig cell tumor, retiform
M8634/1 Sertoli-Leydig cell tumor, intermediate differentiation, with heterologous elements
retiform, with heterologous elements M8634/3 Sertoli-Leydig cell tumor, poorly differentiated, with heterologous elements
M8640/1 Sertoli tumor, NOS
Pick tubular adenoma Sertoli cell adenoma Tubular androblastoma, NOS Testicular adenoma M8640/3 Sertoli cell carcinoma (C62._)
M8641/0 Sertoli cell tumor with lipid storage
Folliculome lipidique (C56.9) Tubular androblastoma with lipid storage Lipid-rich Sertoli cell tumor M8642/1 large cell calcifying Sertoli cell tumor
M8650/0 Leydig cell tumor, benign (C62._)
M8650/3 Leydig cell tumor, malignant
Interstitial cell tumor, malignant M8660/0 Hilus cell tumor (C56.9)
M8670/0 Lipid cell tumor of ovary (C56.9)
Lipoid cell tumor of ovary Steroid cell tumor, NOS Masculinovoblastoma M8670/3 Steroid cell tumor, malignant
M8641/0 Adrenal rest tumor
M8680/0 Paraganglioma, benign
M8680/1 Paraganglioma , NOS
M8680/3 paraganglioma, malignant
M8681/1 Sympathetic paraganglioma
M8682/1 Parasympathetic paraganglioma
M8683/0 Gangliocytic paraganglioma (C17.0)
M8690/1 Glomus jugulare tumor, NOS (C75.5)
Jugular/jugulotympanic paranglioma M8691/1 Aortic body tumor (C75.5)
Aortic/aorticopulmonary paraganglioma M8692/1 Carotid body tumor/paraganglioma (C75.4)
M8693/1 Extra-adrenal paraganglioma, NOS
Nonchromaffin paraganglioma, NOS Chemodectoma M8693/3 Extra-adrenal paraganglioma, malignant
Nonchromaffin paraganglioma, malignant M8700/0 Pheochromocytoma , NOS (C74.1)
Adrenal medullary/chromaffin paraganglioma Chromaffin tumor Chromaffinoma M8700/3 Pheochromocytoma, malignant (C74.1)
Adrenal medullary paraganglioma, malignant Pheochromoblastoma M8710/3 Glomangiosarcoma
M8711/0 Glomus tumor , NOS
M8711/3 Glomus tumor, Malignant
M8712/0 Glomangioma
M8713/0 Glomangiomyoma
M8720/0 Pigmented nevus, NOS
M8720/2 Melanoma in situ
M8720/3 Malignant melanoma , NOS (except juvenile melanoma M8770/0)
M8721/3 Nodular melanoma
M8722/0 Balloon cell nevus
M8722/3 Balloon cell melanoma
M8723/0 Halo nevus
M8723/3 Malignant melanoma, regressing
M8725/0 Neuronevus
M8726/0 Magnocellular nevus (C69.4)
Melanocytoma, eyeball Melanocytoma, NOS M8727/0 Dysplastic nevus
M8727/0 dysplastic nevus
M8728/0 Diffuse melanocytosis
M8728/1 Meningeal melanocytoma (C70.9)
M8728/3 Meningeal melanomatosis (C70.9)
M8730/0 Nonpigmented nevus
M8740/0 Junctional nevus, NOS
M8740/3 Malignant melanoma in junctional nevus
M8741/2 Precancerous melanosis, NOS
M8741/3 Malignant melanoma in precancerous melanosis
M8742/3 Lentigo maligna melanoma
Hutchinson melanotic freckle M8743/3 Superficial spreading melanoma
M8744/3 Acral lentiginous melanoma , malignant
M8745/3 * Desmoplastic melanoma, malignant
M8746/3 Mucosal lentiginous melanoma
M8750/0 Intradermal nevus
M8760/0 compound nevus
Dermal and epidermal nevus M8761/0 Small congenital nevus
M8761/1 Giant pigmented nevus, NOS
Intermediate and giant congenital nevus M8761/3 Malignant melanoma in giant pigmented nevus/congenital melanocytic nevus
M78762/1 Proliferative dermal lesion in congenital nevus
M8770/0 Epithelioid and spindle cell nevus
Juvenile nevus Juvenile melanoma Spitz nevus Pigmented spindle cell nevus of Reed M8770/3 Mixed epithelioid and spindle cell melanoma
M8771/0 Epithelioid cell nevus
M8771/3 Epithelioid cell melanoma
M8772/0 spindle cell nevus, NOS
M8772/3 Spindle cell melanoma, NOS
M8773/3 Spindle cell melanoma, type A
M8774/3 Spindle cell melanoma, type B
M8780/0 Blue nevus, NOS
M8780/3 blue nevus, malignant
M8790/0 Cellular blue nevus
M8800/0 Soft tissue tumor, benign
M8800/3 Sarcoma , NOS
M8800/9 Sarcomatosis, NOS
M8801/3 Spindle cell sarcoma
M8802/3 Giant cell sarcoma (except of bone M9250/3)
M8803/3 Small cell sarcoma
M8804/3 Epithelioid sarcoma
M8805/3 Undifferentiated sarcoma
M8806/3 Desmoplastic small round cell tumor
M8810/0 Fibroma , NOS
M8810/1 Cellular fibroma (C56.9)
M8810/3 Fibrosarcoma , NOS
M8811/0 Fibromyxoma
Myxoid fibroma Myxofibroma, nos M8811/3 Fibromyxosarcoma
M8812/0 Periosteal fibroma (C40._, C41._)
M8813/0 Fascial fibroma
M8813/3 Fascial fibrosarcoma
M8814/3 Infantile fibrosarcoma
M8815/0 Solitary fibrous tumor
M8815/3 Solitary fibrous tumor, malignant
M8820/0 Elastofibroma
M8821/1 Aggressive fibromatosis
Extra-abdominal desmoid Desmoid, NOS Invasive fibroma M8822/1 Abdominal fibromatosis
Abdominal desmoid Mesenteric fibromatosis (C48.1) Retroperitoneal fibromatosis (C48.0) M8823/0 Desmoplastic fibroma
M8824/0 Myofibroma
M8824/1 Myofibromatosis
M8825/0 Myofibroblastoma
M8825/1 Myofibroblastic tumor, nos
Inflammatory myofibroblastic tumor M8826/0 Angiomyofibroblastoma
M8827/1 Myobfibroblastic tumor, peribronchial (C34._)
congenital peribronchial myofibroblastic tumor M8830/0 Benign fibrous histiocytoma
Fibrous histiocytoma, NOS Fibroxanthoma, NOS Xantofibroma M8830/1 Atypical fibrous histiocytoma
M8830/3 Malignant fibrous histiocytoma
M8831/0 Histiocytoma, NOS
Deep histiocytoma Juvenile histiocytoma Reticulohistiocytoma M8832/0 Dermatofibroma, NOS (C44._)
Sclerosing hemangioma Cutaneous histiocytoma Subepidermal nodular fibrosis Dermatofibroma lenticulare M8832/3 Dermatofibrosarcoma, NOS (C44._)
Dermatofibrosarcoma protuberans, NOS M8833/3 Pigmented dermatofibrosarcoma protuberans
M8834/1 Giant-cell fibroblastoma
M8835/1 Plexiform fibrohistiocytic tumor
M8836/1 Angiomatoid fibrous histiocytoma
M8840/0 Myxoma , NOS
M8840/3 Myxosarcoma
M8841/1 Angiomyxoma
M8842/0 Ossifying fibromyxoid tumor
M8850/0 Lipoma , NOS
M8850/1 Atypical lipoma
Superficial well differentiated liposarcoma Well differentiated liposarcoma of superficial soft tissue M8850/3 Liposarcoma , NOS
M8851/0 Fibrolipoma
M8851/3 Liposarcoma, well differentiated
Liposarcoma, differentiated Lipoma-like liposarcoma Sclerosing liposarcoma Inflammatory liposarcoma M8852/0 Fibromyxolipoma
M8852/3 Myxoid liposarcoma
M8853/3 Round cell liposarcoma
M8854/0 Pleomorphic lipoma
M8854/3 Pleomorphic liposarcoma
M8855/3 Mixed liposarcoma
M8856/0 Intramuscular lipoma
Infiltrating lipoma/angiolipoma M8857/0 Spindle cell lipoma
M8857/3 Fibroblastic liposarcoma
M8858/3 Dedifferentiated liposarcoma
M8860/0 Angiomyolipoma
M8861/0 Angiolipoma, NOS
M8862/0 Chondroid lipoma
M8870/0 Myelolipoma
M8880/0 Hibernoma
Fetal fat cell lipoma Brown fat tumor M8881/0 Lipoblastomatosis
Fetal lipoma, NOS Fetal lipomatosis Lipoblastoma M8890/0 Leiomyoma , NOS
Fibroid uterus (C55.9) Fibromyoma Leiomyofibroma Plexiform leiomyoma Lipoleiomyoma M8890/1 Leiomyomatosis, NOS
Intravascular leiomyomatosis M8890/3 Leiomyosarcoma , NOS
M8891/0 Epithelioid leiomyoma
M8891/3 Epithelioid leiomyosarcoma
M8892/0 Cellular leiomyoma
M8893/0 Bizarre leiomyoma
Symplastic/atypical/pleomorphic leiomyoma M8894/0 Angiomyoma
Vascular leiomyoma Angioleiomyoma M8894/3 Angiomyosarcoma
M8895/0 Myoma
M8895/3 Myosarcoma
M8896/3 Myxoid leiomyosarcoma
M8897/1 Smooth muscle tumor of uncertain malignant potential
M8898/1 Metastasizing leiomyoma
M8900/0 Rhabdomyoma , NOS
M8900/3 Rhabdomyosarcoma , NOS
M8901/3 Pleomorphic rhabdomyosarcoma, adult type
Pleomorphic rhabdomyosarcoma, NOS M8902/3 Mixed type rhabdomyosarcoma
Mixed embryonal rhabdomyosarcoma and alveolar rhabdomyosarcoma M8903/0 Fetal rhabdomyoma
M8904/0 Adult rhabdomyoma
M8905/0 Genital rhabdomyoma
M8910/3 Embryonal rhabdomyosarcoma, NOS
Embryonal rhabdomyosarcoma, pleomorphic Sarcoma botryoides Botryoid sarcoma M8912/3 Spindle cell rhabdomyosarcoma
M8920/3 Alveolar rhabdomyosarcoma
M8921/3 Rhabdomyosarcoma with ganglionic differentiation
M8930/0 Endometrial stromal nodule
M8930/3 Endometrial stromal sarcoma, NOS
Endometrial sarcoma, NOS Endometrial stromal sarcoma, high grade M8931/3 Endometrial stromal sarcoma, low grade
Endolymphatic stromal myosis Endometrial stromatosis Stromal endometriosis Stromal myosis, NOS M8932/0 Adenomyoma
Atypical polypoid adenomyoma M8933/3 Adenosarcoma
M8934/3 Carcinofibroma
M8935/0 Stromal tumor, benign
M9835/1 Stromal tumor, NOS
M8935/3 Stromal sarcoma, NOS
M8936/0 Gastrointestinal stromal tumor, benign
M8936/1 Gastrointestinal stromal tumor, NOS
GIST, NOS/uncertain malignant potential Gastrointestinal autonomic nerve tumor (GANT) Gastrointestinal pacemaker cell tumor M8936/3 Gastrointestinal stromal sarcoma
M8940/0 Pleomorphic adenoma
M8940/3 Mixed tumor, malignant, NOS
M8941/3 Carcinoma in pleomorphic adenoma
M8950/3 Müllerian mixed tumor
M8951/3 Mesodermal mixed tumor
M8959/0 Benign cystic nephroma
M8959/1 Cystic partially differentiated nephroblastoma
M8959/3 Malignant cystic nephroma
Malignant multilocular cystic nephroma M8960/1 Mesoblastic nephroma
M8960/3 Nephroblastoma , NOS
M8963/3 malignant rhabdoid tumor
Rhabdoid sarcoma Rhabdoid tumor, NOS M8964/3 Clear cell sarcoma of kidney
M8965/0 Nephrogenic adenofibroma
M8966/0 Renomedullary interstitial cell tumor
M8967/0 Ossifying renal tumor
M8970/3 Hepatoblastoma
M8971/3 Pancreatoblastoma
M8972/3 Pulmonary blastoma
M8973/3 Pleuropulmonary blastoma
M8974/1 Sialoblastoma
M8980/3 Carcinosarcoma, NOS
M8981/3 Carcinosarcoma, embryonal
M8982/0 Myoepithelioma
Myoepithelial tumor Myoepithelial adenoma M8982/3 Malignant myoepithelioma
M8983/0 Adenomyoepithelioma
M8990/0 Mesencymoma, benign
M8990/1 Mesenchymoma, NOS
M8990/3 Mesenchymoma, malignant
Mixed mesenchymal sarcoma M8991/3 Embryonal sarcoma
M9000/0 Brenner tumor , NOS
M9000/1 Brenner tumor, borderline malignancy
Brenner tumor, proliferating M9000/3 Brenner tumor, malignant
M9010/0 Fibroadenoma, NOS
M9011/0 Intracanalicular fibroadenoma
M9012/0 Pericanalicular fibroadenoma
M9013/0 Adenofibroma, NOS
Cystadenofibroma, NOS Papillary adenofibroma M9014/0 Serous adenofibroma, NOS
Serous cystadenofibroma, NOS M9014/1 Serous adenofibroma of borderline malignancy
Serous cystadenofibroma of borderline malignancy M9014/3 Serous adenocarcinofibroma
Malignant serous adenofibroma Serous cystadenocarcinofibroma Malignant serous cystadenofibroma M9015/0 Mucinous adenofibroma, NOS
Mucinous cystadenofibroma, NOS M9015/1 Mucinous adenofibroma of borderline malignancy
Mucinous cystadenofibroma of borderline malignancy M9015/3 Mucinous adenocarcinofibroma
Malignant mucinous adenofibroma Mucinous cystadenocarcinofibroma Malignant mucinous cystadenofibroma M9016/0 Gian fibroadenoma
M9020/0 Phyllodes tumor, benign
Cystosarcoma phyllodes, benign M9020/1 Phyllodes tumor, borderline
Cystosarcoma phyllodes, NOS Phyllodes tumor, NOS M9020/3 Phyllodes tumor, malignant
Cystosarcoma phyllodes, malignant M9030/0 Juvenile fibroadenoma
M9040/0 Synovioma, benign
M9040/3 Synovial sarcoma , NOS
Synovioma, NOS Synovioma, malignant M9041/3 Synovial sarcoma, spindle cell
Synovial sarcoma, monophasic fibrous M9042/3 Synovial sarcoma, epithelioid cell
M9043/3 Synovial sarcoma, biphasic
M9044/3 Clear cell sarcoma, NOS (except of kidney M9864/3)
Clear cell sarcoma, of tendons and aponeuroses Melanoma, malignant, of soft parts M9050/0 Mesothelioma , benign
M9050/3 Mesothelioma , malignant or NOS
M9051/0 Fibrous mesothelioma, benign
M9051/3 Fibrous mesothelioma, malignant or NOS
Spindled mesothelioma Sarcomatoid mesothelioma Desmoplastic mesothelioma M9052/0 Epithelioid mesothelioma, benign
Well differentiated papillary mesothelioma, benign mesothelial papilloma M9052/3 Epithelioid mesothelioma, malignant or NOS
M9053/3 Mesothelioma, biphasic, malignant or NOS
M9054/0 Adenomatoid tumor, NOS
M9055/0 Multicystic mesothelioma, benign
Cystic mesothelioma, benign M9055/1 cystic mesothelioma, NOS
M9060/3 Dysgerminoma
M9061/3 Seminoma, NOS
M9062/3 Seminoma, anaplastic
Seminoma with high mitotic index M9063/3 Spermatocytic seminoma
M9064/2 Intratubular malignant germ cells
Intratubular germ cell neoplasia M9064/3 Germinoma
M9065/3 Germ cell tumor, nonseminomatous
M9070/3 Embryonal carcinoma , NOS
M9071/3 Yolk sac tumor
Endodermal sinus tumor Polyvesicular vitelline tumor Orchioblastoma Embryonal carcinoma, infantile Hepatoid yolk sac tumor M9072/3 Polyembryoma
Embryonal carcinoma, polyembryonal type M9073/1 Gonadoblastoma
M9080/0 Teratoma , benign
Adult cystic teratoma Adult/cystic teratoma, NOS Teratoma, differentiated Mature teratoma M9080/1 Teratoma, NOS
M9080/3 Teratoma , malignant, NOS
Embryonal teratoma Teratoblastoma, malignant Immature teratoma, malignant or NOS M9081/3 Teratocarcinoma
Mixed embryonal carcinoma and teratoma M9082/3 malignant teratoma, undifferentiated
Malignant teratoma, anaplastic M9083/3 Malignant teratoma, intermediate
M9084/0 Dermoid cyst , NOS
M9084/3 Teratoma with malignant transformation
Dermoid cyst with malignant transformation or with secondary tumor M9085/3 mixed germ cell tumor
Mixed teratoma and seminoma M9090/0 Struma ovarii, NOS
M9090/3 Struma ovarii, malignant
M9091/1 Strumal carcinoid
Struma ovarii and carcinoid M9100/0 Hydatidifrom mole, NOS
Hydatid mole Complete hydatidiform mole M9100/1 Invasive hydatidiform mole
Chorioadenoma /destruens Chorioadenoma Invasive mole, NOS Malignant hydatidiform mole M9100/3 Choriocarcinoma , NOS
Chorionepithelioma Chorioepithelioma M9101/3 Choriocarcinoma combined with other germ cell elements
combined with teratoma combined with embryonal carcinoma M9102/3 Malignant teratoma, trophoblastic
M9103/0 Partial hydatidiform mole
M9104/1 Placental site trophoblastic tumor
M9105/3 Trophoblastic tumor, epithelioid
M9110/0 Mesonephroma, benign
Mesonephric adenoma Wolffian duct adenoma M9110/1 Mesonephric tumor, NOS
M9110/3 Mesonephroma, malignant
Mesonephric adenocarcinoma Mesonephroma, NOS Wolffian duct carcinoma M9120/0 Hemangioma , NOS
M9120/3 Hemangiosarcoma
M9121/0 Cavernous hemangioma
M9122/0 Venous hemangioma
M9123/0 Racemose hemangioma
M9124/3 Kupffer cell sarcoma
M9125/0 Epithelioid hemangioma
M9130/0 Hemangioendothelioma , benign
M9130/1 Hemangioendothelioma , NOS
Angioendothelioma Kaposiform hemangioendothelioma M9130/3 Hemangioendothelioma, malignant
Hemangioendothelial sarcoma M9131/0 Capillary hemangioma
Hemangioma simplex Infantile/plexiform/juvenile hemangioma M9132/0 Intramuscular hemangioma
M9133/1 Epithelioid hemangioendothelioma, NOS
M9133/3 Epithelioid hemangioendothelioma, malignant
Intravascular bronchial alveolar tumor M9135/1 Endovascular papillary angioendothelioma
M9136/1 Spindle cell hemangioendothelioma
Spindle cell angioendothelioma M9140/3 Kaposi's sarcoma
Multiple hemorrhagic sarcoma M9141/0 Angiokeratoma
M9142/0 Verrucous keratotic hemangioma
M9150/0 Hemangiopericytoma, benign
M9150/1 Hemangiopericytoma, NOS
Hemangiopericytic meningioma M9150/3 Hemangiopericytoma, malignant
M9160/0 angiofibroma, NOS
Juvenile angiofibroma Fibrous papule of nose Involuting nevus Giant cell or cellular angiofibroma M9161/0 Acquired tufted hemangioma
M9161/1 Hemangioblastoma
M9150/0 Hemangiopericytoma , benign
M9150/1 Hemangiopericytoma , NOS
M9170/0 Lymphangioma , NOS
Lymphangioendothelioma, NOS M9170/3 Lymphangiosarcoma
Lymphangioendothelial sarcoma Lymphangioendothelioma, malignant M9171/0 Capillary lymphangioma
M9172/0 Cavernous lymphangioma
M9173/0 Cystic lymphangioma
Hygroma, NOS Cystic Hygroma M9174/0 Lymphangiomyoma
M9174/1 Lymphangiomyomatosis
M9175/0 Hemolymphangioma
M9180/0 Osteoma , NOS
M9180/3 Osteosarcoma , NOS
Osteogenic sarcoma, NOS Osteochondrosarcoma Osteoblastic sarcoma M9181/3 Chondroblastic osteosarcoma
M9182/3 Fibroblastic osteosarcoma
M9183/3 Telangeictatic osteosarcoma
M9184/3 Osteosarcoma in Paget disease of bone
M9185/3 Small cell osteosarcoma
M9186/3 Central osteosarcoma
Conventional central osteosarcoma Medullary osteo sarcoma M9187/3 Intraosseous well differentiated osteosarcoma
Intraosseous low grade osteosarcoma M9191/0 Osteoid osteoma, NOS
M9192/3 Parosteal osteosarcoma
Juxtacortical osteosarcoma M9193/3 Periosteal osteosarcoma
M9194/3 High grade surface osteosarcoma
M9195/3 Intracortical osteosarcoma
M9200/0 Osteoblastmoa, NOS
M9200/1 Aggressive osteoblastoma
M9210/0 Osteochondroma
M9210/1 Osteochondromatosis, NOS
M9220/0 Chondroma , NOS
M9220/1 Condromatosis, NOS
M9220/3 Chondrosarcoma , NOS
M9221/0 Juxtacortical chondroma
M9221/3 Juxtacortical chondrosarcoma
Periosteal chondrosarcoma M9230/0 Chondroblastoma, NOS
Chondromatous giant cell tumor Codman tumor M9230/3 Chondroblastoma, malignant
M9231/3 Myxoid chondrosarcoma
M9240/3 Mesenchymal chondrosarcoma
M9241/0 Chondromyxoid fibroma
M9242/3 Clear cell chondrosarcoma
M9243/3 Dedifferentiated chondrosarcoma
M9250/1 giant cell tumor of bone, NOS
M9250/3 Giant cell tumor of bone, malignant
Osteoclastoma, malignant Giant cell sarcoma of bone M9251/1 Giant cell tumor of soft parts, NOS
M9251/3 Malignant giant cell tumor of soft parts
M9252/0 Tenosynovial giant cell tumor
Fibrous histiocytoma of tendon sheath Giant cell tumor of tendon sheath M9252/3 Malignant tenosynovial giant cell tumor
Giant cell tumor of tendon sheath, malignant M9260/3 Ewing's sarcoma /tumor
M9261/3 Adamantinoma of long bones
M9262/0 Ossifying fibroma
Fibro-osteoma Osteofibroma M9270/0 Odontogenic tumor, benign
M9270/1 Odontogenic tumor, NOS
M9270/3 Odontogenic tumor, malignant
Odontogenic carcinoma/sarcoma Primary intraosseous or ameloblastic carcinoma M9271/0 Ameloblastic fibrodentinoma
M9272/0 Cementoma, NOS
Periapical cemental dysplasia or cemento-osseus dysplasia M9273/0 Cementoblastoma , benign
M9274/0 Cementifying fibroma
Cemento-ossifying fibroma M9275/0 Gigantiform cementoma
M9280/0 Odontoma, NOS
M9281/0 Compound odontoma
M9282/0 Complex odontoma
M9290/0 Ameloblastic fibro-odontoma
Fibroameloblastic odontoma M9290/3 Ameloblastic odontosarcoma
Ameloblastic fibrodentinosarcoma or fibro-odontosarcoma M9300/0 Adenomatoid odontogenic tumor
M9301/0 Calcifying odontogenic cyst
M9302/0 Odontogenic ghost cell tumor
M9310/0 Ameloblastoma , NOS
Adamantinoma, NOS (except of long bones M9261/3) M9310/3 Ameloblastoma, malignant
Adamantinoma, NOS (except of long bones M9261/3) M9311/0 Odontoameloblastoma
M9312/0 Squamous odontogenic tumor
M9320/0 Odontogenic myxoma
M9321/0 Central odontogenic fibroma
M9322/0 Peripheral odontogenic fibroma
M9330/0 Ameloblastic fibroma
M9330/3 Ameloblastic fibrosarcoma
Ameloblastic sarcoma Odontogenic fibrosarcoma M9340/0 Calcifying epithelial odontogenic tumor
M9341/1 clear cell odontogenic tumor
M9342/3 Odontogenic carcinosarcoma
M9350/1 Craniopharyngioma
M9351/1 Craniopharyngioma, adamantinomatous
M9352/1 Craniopharyngioma, papillary
M9360/1 Pinealoma
M9361/1 Pineocytoma
M9362/3 Pineoblastoma
Mixed pineal tumor Mixed pineocytoma-pineoblastoma Pineal parenchymal tumor of intermediate differentiation Transitional pineal tumor M9363/0 Melanotic neuroectodermal tumor
Retinal anlage tumor Melanoameloblastoma Melanotic progonoma M9364/3 Peripheral neuroectodermal tumor
Neuroectodermal tumor, NOS Peripheral primitive neuroectodermal tumor, NOS (PPNET)
M9365/3 Askin Tumor
M9370/3 Chordoma, NOS
M9371/3 Chondroid chordoma
M9372/3 Dedifferentiated chorcoma
M9373/0 Parachordoma
M9380/3 Glioma, malignant
Glioma, NOS (except nasal glioma, not neoplastic) M9381/3 Gliomatosis cerebri
M9382/3 Mixed glioma
M9383/1 Subepyndymoma
Subependymal glioma Subependymal astrocytoma, NOS Mixed subendymoma-ependymoma M9384/1 Subependymal giant cell astrocytoma
M9390/0 Choroid plexus papilloma, NOS
M9390/1 Atypical choroid plexus papilloma
M9390/3 Choroid plexus carcinoma
Choroid plexus papilloma, anaplastic or malignant M9391/3 Ependymoma , NOS
Epithelial / cellular / clear cell / tanycytic ependymoma M9392/3 Ependymoma, anaplastic
M9393/3 Papillary ependymoma
M9394/1 Myxopapillary ependymoma
M9400/3 Astrocytoma , NOS
Astrocytic glioma Astroglioma Diffuse astrocytoma Astrocytoma, low grade Diffuse astocytoma, low grade Cystic astrocytoma M9401/3 Astrocytoma, anaplastic
M9410/3 Protoplasmic astrocytoma
M9411/3 Gemistocytic astrocytoma
M9412/1 Desmoplastic infantile astrocytoma or ganglioglioma
M9413/0 dysembryoplastic neuroepithelial tumor
M9420/3 Fibrillary astrocytoma
M9421/1 Pilocytic astrocytoma
Piloid or Juvenile astrocytoma Spongioblastoma, NOS M9423/3 Polar spongioblastoma
Spongioblastoma polare Primitive polar spongioblastoma M9424/3 Pleomorphic xanthoastrocytoma
M9430/3 Astroblastoma
M9440/3 Glioblastoma, NOS
M9441/3 Giant cell glioblastoma
M9442/1 gliofibroma
M9442/3 gliosarcoma
Glioblastoma with sarcomatous component M9444/1 Chordoid glioma
Chordoid glioma of third ventricle M9450/3 Oligodendroglioma , NOS
M9451/3 Oligodendroglioma, anaplastic
M9460/3 Oligodendroblastoma
M9470/3 Medullablastoma, NOS
Melanotic medulloblastoma M9471/3 Desmoplastic nodular medulloblastoma
Desmoplastic medulloblastoma Circumscribed arachnoidal cerebellar sarcoma M9472/3 Medullomyoblastoma
M9473/3 Primitive neuroectodermal tumor, NOS
PNET, NOS Central primitive neuroectodermal tumor, NOS (CPNET) Supratentorial PNET M9474/3 large cell medulloblastoma
M9480/3 Cerebellar sarcoma, NOS
M9490/0 Ganglioneuroma
M9490/3 Ganglioneuroblastoma
M9491/0 Ganglioneuromatosis
M9492/0 Gangliocytoma
M9493/0 Dysplastic gangliocytoma of cerebellum (Lhermitte-Duclos)
M9500/3 Neuroblastoma , NOS
Sympathicoblastoma Central neuroblastoma M9501/0 Medulloepithelioma, benign
M9501/3 Medulloepithelioma, NOS
M9502/0 Teratoid medulloepithelioma, benign
M9502/3 Teratoid medulloepithelioma
M9503/3 Neuroepithelioma, NOS
M9504/3 Spongioneuroblastoma
M9505/1 Ganglioglioma, NOS
M9505/3 Ganglioglioma, anaplastic
M9506/1 Central neurocytoma
Neurocytoma Cerebellar liponeurocytoma Lipomatous medulloblastoma Neurolipocytoma Medullocytoma M9507/0 Pacinian tumor
M9508/3 Atypical teratoid/rhabdoid tumor
M9510/0 Retinocytoma
M9510/3 Retinoblastoma , NOS
M9511/3 Retinoblastoma, differentiated
M9512/3 Retinoblastoma, undifferentiated
M9513/3 Retinoblastoma, diffuse
M9514/1 Retinoblastoma, spontaneously regressed
M9520/3 Olfactory neurogenic tumor
M9521/3 Olfactory neurocytoma
M9522/3 Olfactory neuroblastoma
M9523/3 Olfactory neuroepithelioma
Esthesio neuroepithelioma M9530/0 Meningioma, NOS
Microcystic Secretory Lymphoplasmacyte-rich Metaplastic M9530/1 Meningiomatosis, NOS
Diffuse Multiple meningiomas M9530/3 Meningioma, malignant
Anaplastic Leptomeningeal sarcoma Meningeal sarcoma Meningothelial sarcoma M9531/0 Meningothelial meningioma
Endotheliomatous meningioma Syncytial meningioma M9532/0 Fibrous meningioma
M9533/0 Psammomatous meningioma
M9534/0 Angiomatous meningioma
M9537/0 Transitional meningioma
M9538/1 Clear cell meningioma
M9538/3 Papillary meningioma
M9539/1 Atypical meningioma
M9539/3 Meningeal sarcomatosis
M9540/0 Neurofibroma , NOS
M9540/1 Neurofibromatosis , NOS
Multiple neurofibromatosis Von Recklinghausen disease (except of bone) M9540/3 Malignant peripheral nerve sheath tumor
MPNST, NOS MPNST with glandular differentiation Epithelioid with mesenchymal differentiation Melanotic Melanotic psammomatous M9541/0 Melanotic neurofibroma
M9550/0 Plexiform neurofibroma
M9560/0 Neurilemoma, NOS
Schwannoma, NOS Neurinoma Acoustic neuroma Pigmented or melanotic schwannoma Plexiform / cellular / degenerated / ancient / psammomatous M9560/1 Neurinomatosis
M9561/3 Malignant peripheral nerve sheath tumor with rhabdomyoblastic differentiation
MPNST with rhabdomyoblastic differentiation Triton tumor, malignant Malignant schwannoma with rhabdomyoblastic differentiation M9562/0 Neurothekeoma
M9570/0 Neuroma, NOS
M9571/0 Perineurioma, NOS
M9571/3 Perineurioma, malignant
M9560/0 Schwannoma , NOS
M9560/0 Neurinoma
M9560/0 Acoustic neuroma
M9570/0 Neuroma , NOS
M9580/0 Granular cell tumor/myoblastoma, NOS
M9580/3 Granular cell tumor/myoblastoma, malignant
M9581/3 Alveolar soft part sarcoma
M9582/0 Granular cell tumor of thesellar region (C75.1)
M9590/3 MalignantLymphoma , NOS
Lymphoma, NOS Microglioma (C71._) M9591/3 Malignant lymphoma, non-Hodgkin, NOS
Non-Hodgkin's lymphoma , NOSB cell lymphoma, NOS Malignant lymphoma, non-cleaved cell, NOS Malignant lymphoma, diffuse, NOS Malignant lymphoma, lymphocytic, intermediate differentiation, nodular Malignant lymphoma, small cell, noncleaved, diffuse Malignant lymphoma, undifferentiated cell, non-Burkitt Malignant lymphoma, undifferentiated cell type, NOS Lymphosarcoma, NOS Lymphosarcoma, diffuse Reticulum cell sarcoma, NOS Reticulum cell sarcoma, diffuse Reticulosarcoma, NOS Reticulosarcoma, diffuse Malignant lymphoma, small cleaved cell, diffuse Malignant lymphoma, lymphocytic, poorly differentiated, diffuse Malignant lymphoma, small cleaved cell, NOS Malignant lymphoma, cleaved cell, NOS M9596/3 Composite Hodgkin and non-Hodgkin lymphoma
M9650/3 Hodgkin lymphoma, NOS
M9651/3 Hodgkin lymphoma, lymphocyte rich
M9652/3 Mixed cellularity classical Hodgkin lymphoma , NOS
Hodgkin lymphoma, mixed cellularity, NOS M9653/3 Lymphocyte-depleted classical Hodgkin lymphoma , NOS
M9654/3 Hodgkin lymphoma, lymphocyte depletion, diffuse fibrosis
M9655/3 Hodgkin lymphoma, lymphocyte depletion, reticular
M9659/3 Nodular lymphocyte predominant Hodgkin lymphoma
Hodgkin lymphoma, lymphocyte predominance, nodular Hodgkin paragranuloma, NOS Hodgkin paragranuloma, nodular M9661/3 Hodgkin granuloma
M9662/3 Hodgkin sarcoma
M9663/3 Nodular sclerosis classical Hodgkin lymphoma
Hodgkin lymphoma, nodular sclerosis, NOS M9664/3 Hodgkin lymphoma, nodular sclerosis, cellular phase
Classical Hodgkin lymphoma, nodular sclerosis, cellular phase M9665/3 Hodgkin lymphoma, nodular sclerosis, grade 1
Classical Hodgkin lymphoma, nodular sclerosis grade 1 Hodgkin disease, nodular sclerosis, lymphocyte predominance Hodgkin disease, nodular sclerosis, mixed cellularity M9667/3 Hodgkin lymphoma, nodular sclerosis, grade 2
Classical Hodgkin lymphoma, nodular sclerosis, grade 2 Hodgkin disease, nodular sclerosis, lymphocyte depletion Hodgkin disease, nodular sclerosis, syncytial variant 967–969 Mature B-cell Lymphomas[ edit ] M9670/3 Malignant lymphoma, small B lymphocytic, NOS(see also M9823/3)
Small lymphocytic lymphoma Malignant lymphoma, small lymphocytic, NOS Malignant lymphoma, lymphocytic, well differentiated, diffuse Malignant lymphoma, lymphocytic, NOS Malignant lymphoma, lymphocytic, diffuse, NOS Malignant lymphoma, small cell, NOS Malignant lymphoma, small lymphocytic, diffuse Malignant lymphoma, small cell diffuse M9671/3 Malignant lymphoma, lymphoplasmacytic(see also M9761/3)
M9673/3 Mantle cell lymphoma
Includes all variants: blastic, pleomorphic, small cell Mantle zone lymphoma Malignant zone lymphoma Malignant lymphoma, lymphocytic, intermediate differentiation, diffuse Malignant lymphoma, centrocytic Malignant lymphomatous polyposis M9675/3 Malignant lymphoma, mixed small and large cell, diffuse(see also M9690/3)
Malignant lymphoma, mixed lymphocytic-histiocytic, diffuse Malignant lymphoma, mixed cell type, diffuse Malignant lymphoma, centroblastic-centrocytic, NOS Malignant lymphoma, centroblastic-centrocytic, diffuse M9678/3 Primary effusion lymphoma
M9679/3 Mediastinal large B-cell lymphoma (C38.3)
M9680/3 Malignant lymphoma, large B-cell, diffuse, NOS
Diffuse large B-cell lymphoma , NOSMalignant lymphoma, large cell, NOS Malignant lymphoma, large B-cell, NOS Malignant lymphoma, histiocytic, NOS Malignant lymphoma, histiocytic, diffuse Malignant lymphoma, large cell, cleaved and noncleaved Malignant lymphoma, large cell, diffuse, NOS Malignant lymphoma, large cleaved cell, NOS Malignant lymphoma, large cell, cleaved, NOS Malignant lymphoma, large cell, noncleaved, diffuse or NOS Malignant lymphoma, large B-cell, diffuse, centroblastic, NOS Malignant lymphoma, large B-cell, centroblastic, NOS or diffuse Intravascular large B-cell lymphoma Angioendotheliomatosis Angiotropic lymphoma T-cell rich large B-cell lymphoma Histiocyte-rich large B-cell lymphoma Anaplastic large B-cell lymphoma M9684/3 Malignant lymphoma, large B-cell, diffuse, immunoblastic, NOS
Malignant lymphoma, immunoblastic, NOS Immunoblastic sarcoma Malignant lymphoma, large cell, immunoblastic Plasmablastic lymphoma M9687/3 Burkitt lymphoma , NOS(see also M9826/3)
Includes all variants Malignant lymphoma, undifferentiated Malignant lymphoma, small noncleaved Burkitt-like lymphoma M9689/3 Splenic marginal zone lymphoma
M9690/3 Follicular lymphoma , NOS(see also M9675/3)
Malignant lymphoma, follicular/follicle center, NOS M9691/3 Follicular lymphoma, grade 2
Follicular lymphoma, small cleaved cell M9698/3 Follicular lymphoma , grade 3
Malignant lymphoma, large cell/centroblastic, follicular, NOS M9699/3 Marginal zone B-cell lymphoma, NOS
M9700/3 Mycosis fungoides
M9701/3 Sezary syndrome
M9702/3 Mature T-cell lymphoma, NOS
Peripheral T-cell lymphoma , NOST-cell lymphoma, NOS Peripheral T-cell lymphoma, pleomorphic small/medium/large cell/T-zone lymphoma Lymphoepithelioid lymphoma Lennert lymphoma M9705/3 Angioimmunoblastic T-cell lymphoma
Peripheral T-cell lymphoma, AILD (Angioimmunoblastic lymphadenopathy with dysproteinemia) M9708/3 Subcutaneous panniculitis-like T-cell lymphoma
M9709/3 Cutaneous T-cell lymphoma, NOS (C44._)
M9714/3 Anaplastic large cell lymphoma , T cell and Null cell type
Anaplastic large cell lymphoma, CD30+/NOS M9716/3 Hepatosplenic (gamma-delta) cell lymphoma
M9717/3 Intestinal T-cell lymphoma
M9718/3 Primary cutaneous CD 30+ T-cell lymphoproliferative disorder (C44._)
M9719/3 NK/T-cell lymphoma, nasal and nasal type
972 Precursor Cell Lymphoblastic Lymphoma [ edit ] M9727/3 Precursor cell lymphoblastic lymphoma, NOS (see also M9835/3)
M9728/3 Precursor B-cell lymphoblasticLymphoma (see also M9836/3)
M9729/3 Precursor T-cell lymphoblasticLymphoma (see also M9837/3)
M9731/3 Plasmacytoma , NOS
M9732/3 Multiple myeloma (C42.1)
M9733/3 Plasma cell leukemia (C42.1)
M9734/3 Plasmacytoma, extramedullary(not occurring in bone)
M9740/1 Mastocytoma , NOS orExtracutaneous mastocytoma
M9740/3 Mast cell sarcoma
Malignant mast cell tumor Malignant mastocytoma M9741/3 Malignantmastocytosis
M9742/3 Mast cell leukemia (C42.1)
975 Neoplasms of Histiocytes and Accessory Lymphoid Cells [ edit ] M9750/3 Malignant histiocytosis
M9751/1 Langerhans cell histiocytosis , NOS
M9752/1 Langerhans cell histiocytosis, unifocal
Langerhans cell granulomatosis, unifocal Langerhans cell histiocytosis, mono-ostotic Eosinophilic granuloma M9753/1 Langerhans cell histiocytosis, multifocal
Langerhans cell histiocytosis, poly-ostotic M9754/3 Langerhans cell histiocytosis, disseminated
Langerhans cell histiocytosis, generalized Letterer-Siwe disease Acute progressive histiocytosis X M9755/3 Histiocytic sarcoma
True histiocytic lymphoma M9756/3 Langerhans cell sarcoma
M9757/3 Dendritic cell sarcoma , NOS
M9758/3 Follicular dendritic cell sarcoma /tumor
M9760/3 Immunoproliferative disease, NOS
M9761/3 Waldenstrom macroglobulinemia (C42.0) (see also M9671/3)
M9762/3 Heavy chain disease, NOS
Alpha heavy chain disease Mu heavy chain disease Gamma heavy chain disease Franklin disease M9764/3 Immunoproliferative small intestinal disease (C17._)
Mediterranean lymphoma Primary small intestinal extranodal marginal zone lymphoma M9765/1 Monoclonal gammopathy of undetermined significance
MGUS Monoclonal gammopathy, NOS (M9766/1 ) Angiocentric immunoproliferative lesion
M9767/1 Angioimmunoblastic lymphadenopathy
M9768/1 T-gamma lymphoproliferative disease
M9769/1 Immunoglobulin deposition disease
Systemic light chain disease Primary amyloidosis M9800/3 Leukemia , NOS
M9801/3 Acute leukemia , NOS
Blast cell leukemia Undifferentiated leukemia Stem cell leukemia M9805/3 Acute biphenotypic leukemia
M9820/3 Lymphoid leukemia, NOS
M9823/3 B-cell chronic lymphocytic leukemia/small lymphocytic lymphoma (see also M9670/3)
Chronic lymphocytic leukemia , B-cell type (includes all variants of BCLL)Chronic lymphocytic leukemia Chronic lymphoid leukemia Chronic lymphatic leukemia M9826/3 Burkitt cellLeukemia (see also M9687/3)
Acute lymphoblastic leukemia, mature B-cell type M9827/3 Adult T-cell leukemia/lymphoma (HTLV-1 positive) includes all variants
Adult T-cell lymphoma/leukemia M9831/1 T-cell large granular lymphocytic leukemia
T-cell large granular lymphocytosis NK-cell large granular lymphocytic leukemia Large granular lymphocytosis, NOS M9832/3 Prolymphocytic leukemia, NOS
M9833/3 B-cell prolymphocytic leukemia
M9834/3 T-cell prolymphocytic leukemia
M9835/3 Precursor cell lymphoblastic leukemia , NOS (see also M9727/3)
Precursor cell lymphoblastic leukemia, not phenotyped Acute lymphoblastic leukemia , NOS (see also M9727/3)Acute lymphoblastic leukemia, precursor-cell type Acute lymphoblastic leukemia-lymphoma, NOS Acute lymphocytic leukemia Acute lymphoid leukemia Acute lymphatic leukemia Acute lymphoblastic leukemia, L2 type, NOS FAB L2 M9836/3 Precursor B lymphoblastic leukemia (see also M9728/3)
Pro-B ALL Common precursor B ALL Pre-B ALL Pre-pre-B ALL Common ALL c-ALL M9837/3 Precursor T lymphoblastic leukemia (see also M9729/3)
Pro-T ALL Pre-T ALL Cortical T ALL Mature T ALL 984–993 Myeloid Leukemias (C42.1)[ edit ] (9840–9849)Erythroleukemias (FAB-M6 )
M9840/3 Acute myeloid leukemia, M6 type
(9850–9859)Lymphosarcoma cellleukemia (9860–9869)Myeloid (Granulocytic) Leukemias
M9860/3 Myeloid leukemia , NOS
Non-lymphocytic leukemia, NOS Granulocytic leukemia, NOS Myelogenous leukemia , NOSMyelomonocytic leukemia, NOS Myelocytic leukemia, NOS Eosinophilic leukemia Monocytic leukemia, NOS M9861/3 Acute myeloid leukemia, NOS (FAB or WHO type not specified (see also M9930/3)
Acute myelogenous leukemia Acute non-lymphocytic leukemia Acute granulocytic leukemia Acute myelogenous leukemia Acute myelocytic leukemia M9863/3 Chronic myeloid leukemia, NOS
M9866/3 Acute promyelocytic leukemia t(15;17)(q22;q11–12) * Acute promyelocytic leukemia, PML/RAR-alpha
Acute myeloid leukemia, t(15:17(q22;q11–12) Acute promyelocytic leukemia, NOS FAB-M3 (includes all variants)
M9867/3 ) Acute myelomonocytic leukemia
M9870/3 Basophilic leukemia orAcute basophilic leukemia
M9871/3 Acute myeloid leukemia with abnormal marrow eosinophils (includes all variants)
M9872/3 Acute myeloid leukemia , minimallydifferentiated (FAB type M0)
Acute myeloblastic leukemia] M9873/3 Acute myeloid leukemia , without maturation (FAB type M1)
M9874/3 Acute myeloid leukemia , with maturation (FAB M2), NOS
M9875/3 Chronic myelogenous leukemia BCR/ABL positive
Philadelphia chromosome (Ph1 positive) t(9;22)(q34;q11) Chronic granulocytic leukemia (BCR/ABL positive)/(Ph1 positive)/t(9;22)(q34;q11) M9876/3 Atypical chronic myelogenous leukemia BCR/ABL negative
Atypical chronic myeloid leukemia (BCR/ABL negative)/(Ph1 negative) M9891/3 Acute monoblastic and monocytic leukemia
Monoblastic leukemia, NOS FAB M5 (includes all variants) M9895/3 Acute myeloid leukemia multilineage dysplasia
AML with/without prior myelodysplastic syndrome M9896/3 AML with t(8;21)(q22;q22), AML1/ETO
FAB M2 with t(8;21)(q22;q22), AML1/ETO M9897/3 AML with 11q23 (MLL) abnormalities
M9910/3 Acute megakaryoblastic leukemia , NOS
Megakaryocytic leukemia (FAB-M7 ) M9920/3 Acute myeloid leukemia and myelodysplastic syndrome, therapy related , NOSTherapy-related acute myeloid leukemia, alkylating agent/epipodophyllotoxin related
M9930/3 Chloroma orMyeloid sarcoma (see also M9861/3)
M9931/3 )Acute panmyelosis with myelofibrosis (C42.1)
Acute panmyelosis, NOS Acute myelofibrosis Acute myelosclerosis, NOS M9940/3 Hairy cell leukemia (C42.1)
Hairy cell leukemia variant Leukemic reticuloendotheliosis M9945/3 Chronic myelomonocytic, leukemia, NOS
M9946/3 Juvenile myelomonocytic leukemia
M9948/3 Aggressive NK cell leukemia
M9950/3 Polycythemia vera
Polycythemia rubra vera Proliferative polycythemia M9960/1 ChronicMyeloproliferative disease , NOS
M9961/3 Myelosclerosis with myeloid metaplasia
Chronic idiopathicmyelofibrosis Myelofibrosis as a result of myeloproliferative disease Agnogenic myeloid metaplasia Megakaryocytic myelosclerosis Myelofibrosis with myeloid metaplasia M9962/3 Essential thrombocytemia
Idiopathic thrombocythemia Essential/idiopathic hemorrhagic thrombocythemia M9963/3 Chronic neutrophilic leukemia
M9964/3 Chronic eosinophilic leukemia /hypereosinophilic syndrome
997 Other Haematologic Disorders [ edit ] M9970/1 Lymphoproliferative disease/disorder, NOS
M9975/3 Myeloproliferative disease, NOS
M9980/3 Chronic myelomonocytic leukemia orRefractory anemia
M9982/3 Refractory anemia with ringed sideroblasts
M9983/3 Refractory anemia with excess blasts
M9985/3 Refractory cytopenia with multilineage dysplasia
M9986/3 Myelodysplastic syndrome associated with isolated del(5q) chromosome abnormality
M9989/3 Myelodysplastic syndrome , NOS
^ International Classification of Diseases for Oncology; Third edition; World Health Organization; Reprinted 2001; Fritz, Percy, Jack, Shanmugaratnam, Sobin, Parkin, Whelan